Leiomiossarcoma primário de alto grau do pulmão

Primary sarcomas of the lung are rare and account for 0.5% of all primary lung tumors. There were approximately 300 cases described in the literature as of 2006. All histologic types of sarcoma were described, and the most common intrathoracic types reported were angiosarcoma, leiomyosarcoma, fibrosarcoma, hemangiopericytoma, and rhabdomyosarcoma. The biological behavior of these tumors is not well-known due to their low frequency. Leiomyosarcomas represent one of the most common subtypes encountered in the lungs, and usually occur during the sixth decade, with male predominance. Although the frequency of metastatic disease is not related to tumor size, prognosis was reported to be poorer in high-grade tumors. In comparison with other sarcomas, survival after complete resection of pulmonary leiomyosarcoma was reported as longer. We report on a patient with primary leiomyosarcoma originating from the bronchus with complete resection and long-term follow-up. Os sarcomas primarios do pulmao sao raros e representam aproximadamente 0,5% de todas as neoplasias pulmonares. Havia aproximadamente 300 casos descritos na literatura ate 2006. Todos os tipos histologicos foram relatados, sendo que os sarcomas intratoracicos mais comuns sao o angiossarcoma, leiomiossarcoma, fibrossarcoma, hemangiopericitoma e rabdomiossarcoma. Devido a sua baixa frequencia, o comportamento biologico desses tumores nao e bem conhecido. O leiomiossarcoma e um dos subtipos mais encontrados no pulmao, e normalmente ocorre na sexta decada de vida com predominância nos homens. Embora a frequencia de doenca metastatica nao esteja relacionada ao tamanho do tumor, o prognostico e pior nos tumores de alto grau. Quando comparados a outros sarcomas, a sobrevida apos a resseccao completa dos leiomiossarcomas de pulmao e mais prolongada. Relatamos o caso de um paciente com leiomiossarcoma primario de pulmao de origem bronquica tratado com resseccao completa e seguimento de longo prazo.