Síndrome de ventrículo izquierdo hipoplásico: Reporte de una enferma en edad adulta

SummaryH YPOPLASTIC LEFT VENTRICLE SYNDROME . R EPORT OF ACASE IN AN ADULT WOMAN Patients with hypoplastic left heart syndrome with-out surgery dye during the first year of life. In theliterature there is only one report from our institutionof a patient who survived to the second decade oflife without surgery. The purpose of this work is todescribe a case of a 24 years old female withhypoplastic left heart syndrome, who has surviveduntil now in functional class I of New York HeartAssociation without surgery. In our patient, the sur-vival is probably related with the presence of aductus arteriosus, an interatrial septal defect andthe secondary pulmonary arterial hypertension. (Arch Cardiol Mex 2007; 77: 349-353) Palabras clave: Sindrome de ventriculo izquierdo hipoplasico. Paciente adulta. Ecocardiograma. Key words: Hypoplastic left heart syndrome. Adult patient. Echocardiography. complejo corazon izquierdo-aorta. Esto produ-ce una obstruccion significativa del flujo san-guineo e inhabilidad del corazon izquierdo paramanejar la circulacion sistemica. El 25% de lospacientes muere en la primera semana de vida yes poco habitual que sobrevivan despues del mes