Nævus de Becker et hypoplasie hémimaxillaire : association fortuite ou syndrome ?

Summary Introduction Becker's nevus is a dermatological disease sometimes associated with a malformation such as hemifacial bone dysplasia. Observation A 11-year-old male patient presented with a delayed growth of the left maxillary and dental impactions. At 15 years of age, Becker's nevus appeared on the upper torso, both shoulders and cheeks. Le Fort I segmented osteotomy with an iliac bone graft was complicated because of maxillary dysplasia. Discussion The chronology of our patient's cutaneous and maxillary abnormalities was similar to previously reported cases. Conversely, the Becker's nevus–bone dysplasia association has been reported only twice. It may not be a coincidence and could belong to a Becker's nevus syndrome.