Hirschsprung's Disease in Adult Treated by Coloprotectomy and Colo-Anal Anastomosis

Hirschsprung’s disease or congenital aganglionic megacolon, occurs in approximately 1 in every 5000 live births and is about 4 times more frequent in males than in females. Hirschsprung disease is the most frequent aetiology of intestinal occlusion in child. This disease is characterized by lack of ganglionical cells in the submucous membrane and in the myenterical plexuses of the digestive tract in its distal part. Hirschsprung’s disease is a rare pathology Most cases become manifest during the neonatal period, but in rare instances, the disease is initially diagnosed in adult patients.