Hemangioma hemosiderótico targetoide: revisión a propósito de cuatro casos

2009 
El hemangioma hemosiderotico targetoide, conocido tambien como hobnail hemangioma, es un tumor vascular benigno que se localiza preferentemente en tronco y miembros. La forma clasica (o targetoide) se presenta como una papula pequena, solitaria, violacea-amarronada, rodeada por una zona palida y un anillo equimotico periferico. Existe controversia acerca del origen vascular capilar o linfatico de este tumor, aunque estudios inmunohistoquimicos recientes avalan su naturaleza linfatica. Presentamos cuatro casos pediatricos de hemangioma hemosiderotico targetoide con manifestaciones clinicas atipicas.(AU) Targetoid hemosiderotic hemangioma, also known as hobnail hemangioma, is a benign vascular tumor that mainly affects the trunk and limbs. Its classical (or targetoid) appearance is that of a small, solitary, violaceus to brown papule surrounded by a pale halo and a peripheral equimotic ring. Controversy exists about the vascular capillary or lymphatic origin of this tumor; however, recent immuhistochemical studies support its lymphatic nature. We discuss four pediatric cases of targetoid hemosiderotic hemangioma with atypical presentation.(AU)
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