Histiocitoma fibroso maligno de região cervical
2008
Os sarcomas de partes moles (SPM) correspondem a apenas 1% dos tumores malignos. O mais frequente e o histiocitoma fibroso maligno (HFM), caracterizado por invasao e disseminacao metastatica precoce. Nosso objetivo e descrever um caso de HFM submetido a cirurgia e radioterapia adjuvante. Paciente do genero masculino, 49 anos, apresentava massa cervical. A analise histologica evidenciou HFM. Foi submetido a exerese cirurgica da lesao e radioterapia adjuvante. O HFM e um tumor raro que deve fazer parte do diagnostico diferencial das lesoes cervicais primarias. A cirurgia e o tratamento de escolha associado a radioterapia pos-operatoria. Soft tissue sarcomas (STS) accounts for only 1% of malignancies. Malignant fibrous histiocytoma (MFH) is the most frequent, being characterized by invasion and early metastatic dissemination. The aim is to report a MFH case submitted to surgery and postoperative radiotherapy. A 49-year-old man presented neck mass. The histological analysis showed MFH. The patient underwent surgical resection and adjuvant radiation therapy. MFH is a rare tumor that should be part of primary neck lesions differential diagnosis. Surgery is the main treatment associated to radiotherapy.
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