A case of a congenital fibrolipoma of the median region of the maxilla

Congenital lipoma in the oral cavity is very rare. A fibrolipama in the oral cavity of a 40-day-old female infant is reported. A pedunculated tumor measuring 25×15mm was noted at the region from the anterior palate to upper alveolar ridge. Nasal asymmetry due to left deviation of the columella base was present. The patient was admitted and the tumor was resected. A partial bone defect of the midline of the upper alveolar ridge and hard palate were recognized. Pathological examination revealed that the tumor was composed of fat cells and fibrous tissue, and sebaceous glands were present in the submucosal tissue. The pathological diagnosis was a fibrolipoma and histogenetically the tumor seemed to be a hamartoma. A literature-based review of 17 cases of congenital lipoma in the oral cavity is presented. Eleven of these cases were simple lipoma, five fibrolipoma and one was angiolipoma. Two cases of congenital lipoma located in the midline of the upper alveolar ridge, including of our case, had nasal deformity. There may be some relationship between tumor location and nasal deformity.