Pediatric Cutaneous Mucinoses

Primary cutaneous mucinoses are a heterogeneous group of diseases characterized by the abnormal deposition of glycosaminoglycans (mucin) in the skin. They are usually diseases of adult age and are uncommon in children, in whom diagnosis and management are difficult tasks. In particular, the classification of primary cutaneous mucinoses occurring in childhood is a difficult and confusing challenge because of the very limited number of described cases and overlap in their clinicopathological features in the absence of reports of homogeneous case series. Very recently, a classification of primary pediatric cutaneous mucinoses has been proposed.