Carcinoma indiferenciado del maxilar superior tipo rabdoide

espanolEl denominado tumor rabdoide maligno fue individualizado por Haas y cols. como entidad propia, dentro de las neoplasias malignas del rinon, en 1981. A partir de las caracteristicas histopatologicas del mismo fueron documentandose diferentes casos de tumor rabdoide extrarrenal. Tambien se ha reconocido este aspecto en un heterogeneo grupo de neoplasias (carcinoma, melanoma, mesotelioma, y tumores mesenquimales). Microscopicamente, se observa una proliferacion de celulas epitelioides de gran nucleo desplazado por abundantes filamentos intermedios, nucleolos prominentes y abundante citoplasma eosinofilo. En el presente trabajo se documenta el caso de un varon de 50 anos con un tumor maligno del maxilar superior, con caracteristicas histologicas de tumor rabdoide. Se discute su diagnostico diferencial y se revisa la literatura sobre el tema. EnglishThe rhabdoid malignant tumor was individualized by Haas et al. as an independent entity within the kidney malignant neoplasms in 1981. From its histopathological characteristics, different cases of rhabdoid extra-renal tumor were documented.. This aspect has been also recognized in a wide heterogeneous group of tumors (carcinoma, melanoma, mesothelioma and mesenchymal tumors). The diagnosis of extrarenal rahbdoid tumor is based on the presence of a proliferation of epithelioid cells with large nuclei, prominent nucleoli, abundant eosinophilic cytoplasm, and conspicuous cytoplasmic intermediate filaments, which compress the nuclei. In this article we present the case of a 50-year-old male patient with a malignant maxillary tumor with characteristic rhabdoid features. Its differential diagnosis will be discussed. The literature will also be reviewed.