Recurrent submandibular gland swelling as a first manifestation in a child with primary Sjögren syndrome.

: We reported 1 case of primary Sjogren syndrome in a child. The patient complained recurrent submandibular inflammation for more than 2 years without apparent sicca presentations, and Schirmer test resulted negative. However, ultrasound showed hypoechoic areas in the gland, laboratory tests reported the positivity of Sjogren's syndrome A antigen and Sjogren's syndrome B antigen, and biopsy presented periductal lymphocytic infiltration. Therefore, a diagnosis of primary Sjogren syndrome was conducted. Treatment of it required a multidisciplinary team.