Abdominal visceral lesions in von hippel-lindau disease : Incidence and clinical behavior of pancreatic and adrenal lesions at a single center

Introduction Von Hippel-Lindau disease (VHL) is a dominantly inherited multi-system syndrome. Although pheochromocytoma is the hallmark endocrine neoplasm, pancreatic lesions occur frequently, and their management can be complex. This report describes 26 patients from a single institution with pancreatic or adrenal lesions (or both) in the background of VHL.