Mustard Baffle Revision with Systemic Ventricular Assist Device Placement

Abstract Patients with dextro-transposition of the great arteries (D-TGA) who have undergone atrial-level switch procedures often develop systemic right ventricle (RV) failure. An adult with D-TGA with Mustard repair in childhood presented with end-stage heart failure due to systemic RV failure, Mustard baffle leak, and unrepaired partial anomalous pulmonary venous return. She underwent device closure of the baffle leak via catheterization, followed by baffle revision and concomitant systemic ventricular assist device placement by adult and pediatric heart surgeons. This case demonstrates the importance of multi-disciplinary collaboration between pediatric and adult heart failure specialists in caring for complex adult congenital heart patients.