Angiomatosis mesentérica masiva y hemorragia digestiva baja en paciente con síndrome de Klippel-Trenaunay-Weber

Hemogram showed 8.6 mg/dl hemoglobine, 80,000 platelets, and signs of disseminated intravascular coagulation with D dimers at 2000. During physical examination, we found penis varicosities and asymmetric leg hypertrophy (Fig. 1). Colonoscopy and angiography showed massive mesenteric angiomatosis (Fig. 2). An exploratory laparotomy confirmed the previously described findings, showing a massive mesenteric angiomatosis that included the internal and external iliac arteries and veins, which were unresectable (Fig. 3). The patient died a few months after diagnosis from massive intestinal hemorrhage. A diagnosis with Klippel-Trenaunay-Weber syndrome with mesenteric angiomatosis and an associated disseminated intravascular coagulation syndrome that led to angiomatosis (Kassabach-Merrit syndrome) was made.