Duplicación del intestino posterior primitivo: reporte de caso

2010 
Se presenta el caso de una joven de trece anos de edad, quien consulto al servicio de cirugia infantil del Hospital Pablo Tobon Uribe con historia de malformaciones pelvicas desde el nacimiento y colostomia, de cinco anos de evolucion. En el examen fisico presentaba colostomia, fistula anal, duplicaciones de vulva, clitoris, canal vaginal, uretra y tambien doble pliegue intergluteo. Se realizaron diferentes modalidades diagnosticas (cistouretrografia miccional, urodinamia, gammagrafia renal, tomografia y resonancia magnetica) y se hizo el diagnostico de duplicacion del intestino inferior, rara anomalia congenita de la que se cuenta con menos de 50 casos reportados en la literatura. Durante la hospitalizacion se le realizo una correccion quirurgica exitosa de las anomalias encontradas. A 13 y/o female consulted to HPTU PD's surgery department with a history of pelvic malformations since she was born and complaining about a colostomy done five years ago. On clinical examination an anal fistula was seen as well as perineal organs duplicatedincluding: vulva - four labia, clitoris, vaginal canal, urethra, also double gluteal cleft. Several diagnostic modalities were performed (voiding cystourethrography, urodynamic, renalscan, CT and MRI) having a diagnosis of complete duplication of the hindgut and lower urinary tract , a rare congenital anomaly that has fewer than 50 cases reported in the literature. During hospitalization she underwent successful abdominopelvic surgicalcorrection.
    • Correction
    • Cite
    • Save
    • Machine Reading By IdeaReader
    0
    References
    0
    Citations
    NaN
    KQI
    []