Tumor ovárico, células de la granulomatosa juvenil. A propósito de un caso. Hospital Infantil Dr. Robert Reid Cabral (HIRRC), República Dominicana

Granulosa cell ovarian tumors are rare neoplasms, accounting for only 2% to 5% of ovarian tumors. They have an incidence of 1 case / 100,000 women per year. There are 2 subgroups: the adult form and the juvenile. The latter comprises only 5% of all cases and is diagnosed in the first 3 decades of life, between 8 to 9 years and has been seen up to 30 years. Most patients present with localized abdominal pain, bloating, and a palpable mass in the pelvis or abdomen. 10% of cases may debut with an acute abdomen, due to rupture of the tumor and hem peritoneum or due to torsion of the same. Most pre-pubertal patients have isosexual precocious puberty. The tumor is bilateral in 3% of cases, it is generally limited to the ovary at the time of diagnosis. They tend to respond very well to chemotherapy1 2. We present a case of a 5-month-old female from San Jose De Ocoa; Dominican Republic. Which presents a history of progressive increase in breast diameter from the second week of life. The patient was given an external follow-up to our department, where she combined the physical examination with a progressive increase in the abdominal girth coupled with complementary studies that showed free fluid in the abdominal cavity.