Mammae outside Paget disease causing lymphatic edema.

We report a case of extramammary Paget's disease, representing a swollen left leg with reddish maculae on the thigh after resection of primary lesion on scrotum. Histologically, this lesion revealed the lymph duct's ectasis containing the mass of aggregated tumor cells, which were positive by immunohistochemical staining using PAS+Alucian blue, anti-CEA, and anti-c-erbB-2 antibodies. These were compatible with those of Paget's disease. Clinical appearance and histological findings of reddish lesion seen in this patient might be one of the characteristics of metastasis and infiltration of Paget's cells to lymph ducts.