Dandy–Walker Syndrome: Management at Acharya Vinoba Bhave Rural Hospital, Wardha, India

We discuss 10 cases of Dandy–Walker syndrome that presented between May 2014 and June 2015 at the Department of Neurosurgery and General Surgery in Acharya Vinoba Bhave Rural Hospital, Sawangi (M), Wardha, India. As the definitive surgical treatment protocol is not standardized, we discuss the different techniques used. Combined cystoperitoneal (CP) and ventriculoperitoneal (VP) shunt was done in three cases, two were treated with CP shunt alone, and the remaining five cases were managed with VP shunt. Follow-up showed marked reduction in the head circumference and better motor development, along with alleviation of other neurological symptoms. Seizures, hearing or visual problems, various central nervous system abnormalities, and systemic abnormalities were associated with poor intellectual development and could be used to predict intellectual outcome. Prognosis varies due to several factors, but an early diagnosis and appropriate treatment have a good prognostic value.