ТРУДНОСТИ РАННЕЙ ДИАГНОСТИКИ И ОПЕРАТИВНОЙ КОРРЕКЦИИ ТЯЖЕЛОГО ВРОЖДЕННОГО ПОРОКА СЕРДЦА – ОБЩЕГО ОТКРЫТОГО АТРИОВЕНТИКУЛЯРНОГО КАНАЛА У РЕБЕНКА ПЕРВОГО ГОДА ЖИЗНИ

The common open atrioventricular canal (COAVС) or atrioventricular septal defect (AVSD) includes a large group of anomalies combined by one anatomical symptom: a deficit of muscle and membranous atrioventricular septum (AV-septum) from the interatrial septum fenestration to a functional single ventricle. This defect is 4% of all congenital heart diseases. In 75% of patients with COAVC Down syndrome is noted. The clinical case of a child with COAVC, combined with Down syndrome is described. After a thorough examination, clarification of the diagnosis, the child underwent an operative correction of this defect according to the modified “Australian” technique. The authors draw attention to the difficulties of early diagnosis of severe congenital heart disease.