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Hemangioma pulmonar esclerosante

2009 
O hemangioma pulmonar esclerosante e um tumor pouco frequente, que se manifesta como nodulo pulmonar solitario. Entretanto, o seu comportamento biologico ainda nao esta definido adequadamente. O diagnostico e a evolucao dessas lesoes sao dificultados pelos achados radiologicos inespecificos e a dificuldade de interpretacao das biopsias de congelacao. Os autores descrevem um caso em que o tumor foi completamente retirado com a lobectomia, e o diagnostico histopatologico definitivo foi de hemangioma esclerosante de pulmao. A resseccao em cunha e realizada na maioria dos casos; porem, quando o diagnostico nao e definido no intra-operatorio, e recomendada resseccao mais extensa e linfadenectomia sistematica. Mais estudos sao necessarios para avaliar a extensao da doenca, apesar das metastases nao alterarem o excelente prognostico. Lung sclerosing hemangioma is an uncommon tumor that presents as a solitary asymptomatic nodule. However, the biologic behavior of this tumor has not yet been characterized adequately. Diagnostic evaluation of this lesion is a diagnostic challenge due to the nonspecific radiological findings, potential intraoperative dilemmas like difficult frozen section interpretation.We describe a case of lung sclerosing hemangioma. The tumour was completely removed by lobectomy and the definitive biopsy was informed as a lung sclerosing hemangioma. Generally, wedge resection is justified in the majority of cases, but in cases of uncertain intraoperative diagnosis, extensive resection with systematic lymphadenectomy is recommended.More studies are needed to evaluate extension of this disease, despite metastasis does not seem to change theexcellent prognosis.
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