Papillary renal cell carcinoma associated with autosomal dominant polycystic kidney disease

A case of papillary renal cell carcinoma in a patient suffering from autosomal dominant polycystic kidney disease is described. The occurrence of papillary renal cell carcinoma in polycystic kidneys in the literature is reviewed and the implications of operative management and further surveillance in case of a papillary renal cell carcinoma are discussed.