Mucosa-related Lymphoid Tissue Lymphoma of the Parotid Gland-Case Report and Literature Review

Background:Mucosa-related lymphoid tissue (MALT) lymphomas are rare low-grade B-cell lymphomas, mostly arising from the gastrointestinal tract. MALT lymphomas arising from the parotid gland are very rare.Aim and objective:We report the rare condition of mucosa-related lymphoid tissue lymphoma arising from the parotid gland and discuss their treatment and outcome.Material and Methods:A 77-year-old man presents with a 10-month history of a slow growing painless tumor at his right periauricular area. It measured 4 x 3 cm in size. There were another two palpable tumors at lower pole of the parotid gland, with the largest one measuring 1.7cm. After excisional biopsy of the minor tumors at the lower pole. The pathology confirmed MALT lymphoma. Superficial parotidectomy with concurrent radiation therapy was done.Results:There was no evidence of local recurrence and distant metastasis on the 11 months follow-up.Conclusion:Mucosa-associated lymphoid tissue lymphoma is rarely arising from the parotid gland. Diagnosis of the disease is very difficult and should be suspected if a patient has significant risk factors. Conservative superficial parotidectomy is recommended both for diagnosis and treatment. Radiation therapy is recommended for limited stages of the disease with systemic chemotherapy advised for advanced stage. Prognosis is favorable with careful post-treatment follow-up.