A LOW GRADE TUMOR, EXTRA SKELETAL MYXOID CHONDROSARCOMA, WITH METASTATIC POTENTIAL: A CASE REPORT

Extraskeletal Myxoid Chondrosarcoma (EMC) is a rare soft tissue sarcoma of uncertain differentiation characterized by abundant myxoid matrix located in the soft tissues. It affects mainly the soft tissues of the proximal end of long bones. EMC has a male preference, and this occurs in soft tissue area in patients who are more than 40 years old. The present case was 63 year old female diagnosed as EMC on histopathological examination with immuno–histochemical confirmation and after eight months presented with pulmonary and inguinal metastasis. EMC is a rare tumor should be considered in the differential diagnosis of myxoid soft tissue neoplasm. Therefore, a multi-modal approach, having distinct clinical, cytological, histo-pathological, immunohistochemical features and cytogenetics analysis, must be necessary in establishing a more definitive diagnosis, which may finally lead to a more targeted and specific treatment for patients.         Keywords: Extraskeletal myxoid chondrosarcoma, Inguinal metastasis, low grade tumor, IHC