Síndrome de Mayer-Rokitansky-Kuster-Hauser (SMRKH): relato de caso

Relata-se o caso clinico de paciente feminino, 46 anos de idade, que procurou, ha 21 anos, atendimento medico, apos varias tentativas frustradas de engravidar. Nao havia levado em consideracao que sua menarca nao tinha acontecido, o que ocorreu talvez a sua pouca informacao. Trata-se da sindrome de Mayer-Rokitansky-Kuster-Hauser. A obtencao do diagnostico exigiu intensa propedeutica, como ultrassonografia abdominal total e pelvica endovaginal, laparotomia exploradora e urografia excretora. Nao ha consenso quanto ao melhor acesso terapeutico. A paciente nao foi submetida a qualquer das formas terapeuticas. We report a case of female patient, 46 years old, who began to seek medical attention at age 25, after several failed attempts to become pregnant. Still did not take into account that her menarche had not occurred. This fact is perhaps due to little information about the patient. This is the syndrome of Mayer-Rokitansky-Kuster- Hauser. Obtaining the required extensive diagnostic workup, as USG total abdominal + pelvic endovaginal, laparotomy and intravenous urography. Currently there is no consensus on the best therapeutic access. The patient was not subjected to any form of treatment.