Alopecia fibrosante frontal. Estudio de 12 casos en la Argentina
2018
La alopecia fibrosante frontal (AFF) es una alopecia cicatrizal primaria que tipicamente afecta a mujeres posmenopausicas y se caracteriza por la recesion de la linea de implantacion pilosa fronto-parieto-temporal, con perdida total o parcial de las cejas. Es una entidad de curso cronico y de evolucion incierta. No hay actualmente criterios de evaluacion clinico-pronostica validados a nivel internacional, aunque hace poco se ha propuesto una clasificacion para tal fin basada en una gran casuistica multicentrica. Objetivo: Describir las caracteristicas clinicas de las pacientes con diagnostico de AFF evaluadas en dos centros argentinos. Diseno: Estudio retrospectivo de 12 pacientes con AFF evaluadas entre agosto de 2015 y agosto de 2017 en el Servicio de Dermatologia del HIGA Eva Peron (San Martin, Provincia de Buenos Aires) y en un centro medico privado (General Pico, La Pampa). Materiales y metodos: Se tomaron como criterios de inclusion la presencia de recesion fronto-parieto-temporal de la linea de implantacion pilosa asociada a uno de los siguientes: cambios dermatoscopicos caracteristicos de AFF (eritema e hiperqueratosis perifoliculares y cierre de aperturas foliculares) o una biopsia del cuero cabelludo compatible con alopecia cicatrizal linfocitica. Resultados: Se evaluaron 12 pacientes en 2 anos, todas mujeres menopausicas y con una edad promedio en el momento del diagnostico de 69 anos. La afectacion de las cejas total o parcial se observo en el 100% de los casos. El patron clinico mas frecuente fue el lineal (75%), seguido del difuso (17%). Todas estaban en tratamiento con inhibidores de la 5α-reductasa y minoxidil al 5% topico, y 42% recibian periodicamente infiltraciones con triamcinolona. Conclusiones: La cohorte estudiada presento una edad promedio de diagnostico mas alta que la informada, pero con caracteristicas clinicas similares a las publicadas en la literatura medica internacional. Limitaciones: El caracter retrospectivo del estudio y el tamano de la muestra. Palabras clave: Alopecia fibrosante frontal, liquen plano pilar, alopecia cicatrizal, PPAR, pioglitazona, dutasterida. Dermatol. Argent. 2018, 24 (2): 97-102 Frontal fibrosing alopecia. A study of 12 cases in Argentina Frontal fibrosing alopecia (FFA) is a primary scarring alopecia that typically affects postmenopausal women and is characterized by the recession of the frontal-parieto-temporal hairline with total or partial loss of eyebrows. It is an entity of chronic course with uncertain evolution. There are currently no internationally validated clinical-prognostic evaluation criteria, although a classification for this purpose has recently been proposed based on a large multicentric casuistry. Objective: To describe the clinical and demographic characteristics of patients diagnosed with FFA assessed in two Argentine centers. Design: Retrospective study of 12 patients with FFA evaluated between August 2015 and August 2017 at the Dermatology Service of HIGA Eva Peron (San Martin, Provincia de Buenos Aires) and a private medical center (General Pico, La Pampa). Materials and methods: The inclusion criteria was the presence of frontal-parietol-temporal recession of the hair implantation line associated to one of the following: characteristic changes of FFA (perifollicular erythema and hyperkeratosis and closure of follicular openings) and/or scalp biopsy compatible with lymphocytic scar alopecia. Results: Twelve patients were evaluated in 2 years. All female, menopausal and with average age of diagnosis 69 years. Total or partial eyebrows involvement was observed in 100% of cases. The most frequent clinical pattern was the linear pattern (75%) followed by diffuse pattern (17%). All were treated with 5-alpha reductase inhibitors and topical minoxidil and 42% received periodic intralesional triamcinolone. Conclusions: The cohort studied presented a mean age of diagnosis higher than the reported, but with clinical characteristics similar to those published in the international literature. Limitations: The retrospective nature of the study and the size of the sample. Keywords: Frontal fibrosing alopecia, lichen planopilaris, cicatricial alopecia, PPAR, pioglitazone, dutasteride. Dermatol. Argent. 2018, 24 (2): 97-102
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