Atrial flutter radiofrequency ablation in the setting of left isomerism and repaired single atrium: first case.

Left isomerism is a form of heterotaxy syndrome, characterized by intracardiac defects and caval venous variations, associated with an abnormal arrangement of bronchi and abdominal organs.1 Left isomerism is defined by symmetrical left anatomy of the atria and bronchi.2 Conduction abnormalities and atrial arrhythmias are known manifestations of this condition. However, to the best of our knowledge, atrial flutter is seldom associated with this anomaly.3 We here report for the first time a case of atrial flutter successfully treated by radiofrequency ablation in the setting of left isomerism and repaired single atrium.