CARDIAC FIBROMA AS MANIFESTATION OF NEVOID BASAL CELL CARCINOMA SYNDROME

Cardiac fibromas occur in 3% of patients with nevoid basal cell carcinoma syndrome (NBCCS), an autosomal dominant disorder characterized by multiple basal cell carcinomas, intracranial dural calcifications (Figure 1A), and odontogenic keratocysts (Figure 1B-C). Early diagnosis is essential for