Congenital Absence of Gall Bladder.

Although biliary system variants are extremely common, isolated congenital absence/agenesis of gall bladder (AGB) is extremely rare, with a reported incidence ranging between 0.013 and 0.075% [1]. More than 50% of the patients with AGB are symptomatic for biliary tract disease and require some form of surgical intervention [1]. Inspite of all available diagnostic modalities pre-operative diagnosis of AGB may be illusive and present a surprise to the abdominal surgeon at laparotomy. We present a case of AGB who presented with features of obstructive jaundice and at operation was found to have AGB with choledocholithiasis.