Leiomyosarcoma of the pulmonary artery

Abstract Successful resection of a pulmonary artery leiomyosarcoma was performed in a patient with clinical features of chronic pulmonary embolism. With radical radiotherapy to the mediastinum and solitary right hip metastasis, the patient remained well 6 months later. The difficulty of accurate diagnosis is considered in the light of recent advances in the techniques of cardiac investigation.