Calcinosis cutis idiopática: presentación de 8 casos

2014 
La calcinosis cutis idiopatica (CCI) es una afeccion dermatologica poco frecuente en pediatria, caracterizada por la presencia de nodulos cutaneos calcificados, sin evidencia de lesiones tisulares previas o defectos metabolicos subyacentes. Afecta por igual a ambos sexos y su tratamiento depende del grado de compromiso estetico o funcional. Presentamos 8 ninos con lesiones de CCI. Hubo un leve predominio de afectacion del sexo femenino, y la edad promedio de presentacion fue de 5 anos. Las lesiones se ubicaron preferentemente en la cara, en coincidencia con lo relatado en la literatura. Si bien es una patologia benigna, existen muchos diagnosticos diferenciales, por lo que creemos que publicar nuestra experiencia podria ayudar a considerar su diagnostico en la practica diaria y asi evitar la realizacion de estudios complejos innecesarios. (AU) Idiopathic calcinosis cutis (ICC) is a rare pediatric condition characterized by the presence of skin calcified nodules without evidence of previous tissue injury or underlying metabolic defects. It affects both sexes equally and treatment depends on the aesthetic or functional compromise. We herein present 8 children with lesions of ICC. A slight female predominance was observed and the median age of presentation was 5 years. Lesions were located mainly on the face, in accordance with the reported data in the literature. Although it is a benign disease, many differential diagnoses must be considered, therefore we believe that publishing our experience may help to consider its diagnosis in daily practice and avoid performing unnecessary complex studies. (AU)
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