CASE REPORT OF A 17 - YEAR OLD GIRL WITH ATYPICAL CLINICAL PRESENTATION OF - ARRHYTHMOGENIC RIGHT VENTRICULAR CARDIOMYOPATHY

We report a case of a 17-year-old girl diagnosed with arrhythmogenic right ventricular cardiomyopathy (ARVC), who has been wrongly considered as having idiopathic ventricular extrasystoles for 13 years. The only noteworthy clinical finding until the final diagnosis was made, were complex ventricular arrhythmias (VA) during exercise as well as nonspecific repolarisations changes in inferolateral leads. We would like to increase paediatricians alertness to children presenting with so called “idiopathic” exercise induced VA that at time could turn out to be markers of arrhythmogenic condition. Key words: arrhythmogenic right ventricular cardiomyopathy, ventricular arrhythmias