Enfermedad de Castleman de localizacion cervical

2007 
espanolLa enfermedad de Castleman se caracteriza por la presencia de masas de tejido linfatico; existen dos variedades, la hialino vascular 91% (localizada) y plasmatica 9% (multicentrica). Presentamos un varon de 30 anos con tumoracion latero cervical izquierda indolora. Se realizo una exeresis total de la lesion. La histologia de enfermedad de Castleman variante hialino vascular. La enfermedad de Castleman se presenta fundamentalmente en el tejido linfatico mediastinico. La localizacion cervical es muy rara. Se debe realizar un estudio de extension para descartar la forma multicentrica de la enfermedad. En la forma localizada la extirpacion de la lesion implica la curacion de la enfermedad. EnglishCastleman's disease is characterized by the presence of lymphatic tissue masses. The are two forms, the hyaline vascular 91% (unifocal) and the plasmatic 9% (multifocal). We present a 30 year old man with a left laterocervical painless mass. Total resection of the tumor was performed. The histological result was Castleman's disease hyaline vascular form. Castleman's disease present mainly in the lymphatic tissue of the mediastinum. Cervical location is very rare. Periphery metastasis work up must be done to rule out the multifocal form of the disease. Surgical excision is curative for the unifocal form.
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