INTERMEDIATE TYPE OF BURKITT'S LYMPHOMA: A RARE CASE REPORT.

INTRODUCTION Burkitt lymphoma(BL) is a highly aggressive lymphoma first described by Dennis Parsons Burkitt in 1958.It is a childhood tumor but can also be seen in adults. Among Indian population it is a very rare malignancy accounting for only 0.76% of solid malignant tumor. There are three distinct forms of BL –:a) the endemic or African form, found in equatorial Africa and Papua New Guinea, b) the non endemic or sporadic form, found in areas such as North America, Northern and Eastern Europe and the Far East and Immunodeficiency associated form. An intermediate form may also be distinguished, and this occurs in areas such as Southern Europe, the Middle East and parts of SouthAmerica. Endemic form has a peak incidence in children between 3 and 8 years of age. Common site of disease presentation is the face, with multiple facial bone involvement. Sporadic form affects the older children, with mean age of 11 years. It is more likely to have leukemic or bone marrow involvement, and less likely to have jaw involvement. Common site of involvement beingabdomen. The distinction between different types is generally based on geographic location, association with Ebstein barr virus (EBV), clinical presentation, incidence, age at presentation and sex ratio. BL in India could be a variation between sporadic and endemic types in its clinical presentation. Here, we present a rare case report of sporadic form of Burkitt’s Lymphoma occurring in a young Indian boy presenting with the features of endemic Burkitt’s lymphoma.