Dissecting aortic aneurysm with Marfan syndrome.

Examination revealed an asthenic built child with height of 162 cm, arm span 174 cm, arm span-toheight ratio 1.074 and US:LS ratio 0.82. He had high arched palate, arachnodactly, positive wrist and thumb signs. There were signs of consolidation over left base. Cardiovascular system examination revealed a short diastolic murmur in aortic space. Skiagram revealed a massive consolidation of left lower zone. Clinical and radiological features of consolidation resolved following antibiotic therapy. However repeat radiological evaluation revealed an underlying mediastinal widening. High resolution computerized tomography revealed a large aortic aneurysm (Fig. 1). Color Doppler revealed aortic dilatation just after the origin of left subclavian artery and a large intimal flap just before the origin of superior mesenteric artery.