AMYOPLASIA CONGENITA IN A PREMATURE BABY

Aim: Arthrogryposis multiplex congenita is a term used to describe the multiple joint contractures at birth. Amyoplasia congenita in clinic, hands and wrist are in flexion, elbows are in extension, shoulder are in adduction and internal rotation, bilateral pes equinovarus deformity and multiple joint contractures are present. Amyoplasia is the most common sub-group of arthrogryposis multiplex congenita. The pathogenesis of the disease is not known. Early diagnosis, early treatment is important to launch. Herein, we present a 10-month old infant with multiple joint contractures at premature birth with a diagnosis of amyoplasia congenita. Amyoplasia is a rare condition in premature baby. It is the purpose of this report to summarize and update what is known about the etiology, comorbid disorder, and orthopaedic approach of infants with this diagnose.