Clinical picture and diagnosis of systemic angioreticulomatosis

: Among 131 patients with angioreticulomas of different parts of the central nervous system 16 and systemic angioreticulomatosis, which in half of the patients was in the form of multifocal lesion within the boundaries of the central nervous system, and in the remaining patients, in the form of the Hippel-Lindau syndrome. The authors point out frequent recurrence of this pathological condition, relatively poor results of surgical treatment, and the difficulty of intravital diagnosis, particularly in the case of asymptomatic visceral pathology in the Hippel-Lindau disease. The complex of diagnostic measures included total computer tomography which allowed systemic angioreticulomatosis to be verified in different stages of its clinical development. The clinical, computer-tomographic, and post-mortem findings in systemic angioreticulomatosis are compared.