Melanotic neuroectodermal tumor of infancy: A rare presentation of an extremely rare neoplasm and diagnostic implications in Gombe, Nigeria

Melanotic neuro-ectodermal tumor of infancy is very rare. A unique neoplasm of the formative years, it typically involves the face or cranium; possesses rapid, expansile growth; presents as a firm swelling and displays a high rate of recurrence. Its rarity and unique features make diagnosis and management quite challenging. This challenge is increased in resource-limited settings like ours and with atypical presentation, such as was seen at our center, where patient presented with a bony hard swelling. Key words : Melanotic neuro-ectodermal tumor of infancy, benign tumor, maxillary tumor, infant, bony-hard swelling, firm swelling, diagnostic challenges, management  challenges, vanyl mandellic acid, wide excision