Type 1-segmentale morbus Darier

Darier Disease (DD) is a rare autosomal dominant genetic skin disorder. Characteristic skin changes consist of symmetrically distributed red to brown hyperkeratotic papules and plaques. Mosaicism has been described in DD in which the skin disorder shows a segmental distribution. In this article we report a 64-year-old patient diagnosed with type 1 localized Dariers disease based on the clinical and histopathological features. In addition, we review the pathogenesis and therapeutic modalities of localized DD.