Dental Treatment of 49,XXXXY Syndrome: A Case Report

A bstr A c t A 12-year-old male patient with 49,XXXXY syndrome is presented, who was treated under general anesthesia due to mental retardation and uncooperative behavior. The child was treated as an emergency case in two occasions due to severe pain and abscesses. Several teeth were severely decayed and had to be extracted resulting in extensive anodontia as there was no secondary dentition to follow. This case emphasizes the importance of regular dental care, good nutrition and monitoring of dental development in children with 49,XXXXY syndrome.