Erken cerrahi tedaviden fayda gören bir Sturge - Weber sendromu olgusu

In Sturge-Weber syndrom in case the seizures accompany in early infontile period, the occurrence of earlier hemiparesis, resistant hemiparesis and progressive motor mental retardation is well-established . Recently, surgical intervention has been proposed as a treatment option in such cases. This study presents a Sturge-Weber case who presented with resistant complex partial seizures and underwent a successful left functional hemispherectomy. A 21-month-old girl was presented to our hospital with right-localized seizures the onset of which was 2.5 months of age. The seizures which had occured as many as 10 times a day had caused status in the course of diseases accompanied by high fever. Physical exam revealed right hemiparesis, microcephaly, and a hemangioma located on left side of her face and on her neck. Angioma and gliosis were detected on left cerebral hemisphere temporooccipital lobe by brain magnetic resonance imaging. Although phenobarbital, carbamazepine and valproate had been given at maximal doses, these treatments did not help and the patient was hospitalized for 6 more times with status before she underwent left functional hemispherectomy. The patient has been under follow-up with lower doses of antiepileptics after the surgery and she has not had a seizure since then.