Palpitations Revealing A Primary Pulmonary Artery Sarcoma

Abstract Primary pulmonary artery sarcoma is an exceedingly rare and aggressive malignancy that carries poor prognosis. Clinical manifestations are non-specific and include chest pain, dyspnea, syncope, palpitations and asthenia among others. Delay to diagnosis is common and compromises the prognosis. Here we report an interesting case of primary pulmonary artery sarcoma presenting with frequent monomorphic premature ventricular contractions arising from the right/left ventricle outflow tract. Cardiac imaging is key in the evaluation of patients with frequent premature ventricular contractions to rule out rare pathologies such as tumour compression.