Surgical treatment of complex congenital heart diseases with extracardiac conduit total cavopulmonary connection

Objective To report the experience of extracardiac conduit total cavopulmonary connection (ECTCPC) in surgical treatment of complex congenital heart diseases.Methods From 1998 to 2006,68 patients underwent ECTCPC for complex congenital heart diseases.Among them,45 had functional univentricle with transposition of the great artery (TGA) and pulmonary artery valve stenosis,19 had tricuspid atresia with hypoplasia of right ventricle,4 had Ebstein's anomaly with hypoplasia of right ventricle.Six had left superior vena cava,18 had received Bidirectional Gleen operation;Fifty-seven cases were performed under cardiopuhnonary bypass with general anesthesia and hypothermia,11 cases were performed without cardiopulmonary bypass.Results There were two death,the mortality was 2.9%.All patients were followed up from 1 to 8 years with no clinical symptoms and have been doing well.The arterial oxygen saturation was 90%-96%,the cardiac function were in NYHA class Ⅰ-Ⅱ.Conclusion The extra cardiac conduit TCPC is a simple procedure and superior to other type of Fontan procedure in most