Management of an infant with congenital Factor VII deficiency presenting with obstructed inguinal hernia

Surgery on an infant with factor VII deficiency is a risky affair, more so when the infant is premature and low birth weight. A 2-month-old infant with factor VII deficiency presented with obstructed right inguinal hernia. He had features suggestive of intestinal obstruction. The hernia was reduced, and the infant was initially managed conservatively. He was operated upon after 72 h under cover of recombinant activated factor VII concentrate to control the bleeding and was closely monitored for bleeding in the postoperative period. After confirming optimal wound healing and no recurrence on 6-month follow-up, contralateral herniotomy for a reducible inguinal hernia was performed at the age of 9 months. Even on thorough literature search, no references have been found on the management of an infant with this rare coagulation disorder undergoing herniotomy during early infancy. Hence, the case is being reported.