POOR OUTCOME OF ATYPICAL TERATOID RHABDOID TUMOR OF BRAIN IN AN ADULT PATIENT TREATED WITH PAEDIATRIC PROTOCOL

Atypical teratoidrhabdoid tumor (ATRT) of the CNS is an extremely rare and aggressive tumor of early childhood with generally poor outcome even with multimodality treatment 1, 2. Usually it presents in children less than 2 years with posterior cranial fossa being the most common site 2. ATRT is extremely rare in adults with just over 30 cases reported in literature 3.Here we present a case of ATRT in an adult patient who presented with tumor in temporal region. Even with gross total excision of tumor and multimodality treatment he had progressive disease and succumbed to his illness. This case is presented for rarity of disease and to highlight difficulties in implementation of pediatric protocol for treatment of adult patients with ATRT.