Congenital segmental dilatation of the colon

: Segmental dilatation of the colon is a rare congenital entity that cause chronic constipation in children. A new case is presented and another 9 former cases described in the literature are reviewed. We think that this entity may be diagnosed before the operation, if it is kept in mind. So, the barium enema and rectal biopsy are of paramount importance. The resection of the dilated ++ segment is the treatment of choice.