Enfermedad de Behcet: Informe de 5 casos

1998 
Se estudiaron 5 sujetos con enfermedad de Behcet segun los criterios establecidos para detectarla. Se encontraron ulceras orales en todos; las lesiones en genitales, en 4; el eritema nudoso, en 3; la patergia, en 3; la artritis, en 2; la oclusion vascular, en 2; las lesiones papulopustulosas y piodermicas, en 3; y lesiones acneiformes, en 1. No hubo lesion ocular de las senaladas como criterio en ninguno de los pacientes objeto de estudio, pero si conjuntivitis angular bilateral cronica en uno. En otro enfermo se observo la asociacion de esta entidad con la policondritis recidivante (sindrome MAGIC), el cual constituye el primer caso reportado en Cuba. 5 patients suffering from Behcet´s syndrome were studied according to the criteria established to detect it. Oral ulcers were observed in all of them, genitalia lesions, in 4; nodose erythema, in 3; pathergy, in 3; arthritis, in 2; vascular occlusion, in 2; papulopustular and pyodermal lesions, in 3; and acneiform lesions, in 1. There was no ocular lesion of those considered as criterion in any of the patients under study, but chronic bilateral angular conjunctivitis was found in one of them. It was observed the association of this disease with recidivist polychondritis (MAGIC syndrome) in another patient that is the first case reported in Cuba.
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