Esclerose sistêmica difusa grave: relato de caso em homem

Homem de 64 anos se apresentou no servico de emergencia relatando espessamento progressivo da pele, lombalgia, disfagia e lesoes necroticas dolorosas em quirodactilos. Foi feito o diagnostico de esclerose sistemica difusa grave, com insuficiencia renal cronica, fibrose pulmonar e miocardiopatia secundarias a esclerodermia. Sao discutidas a manifestacao grave dessa doenca, suas complicacoes e apresentacao no sexo masculino. A 64-year-old male presented at the emergency unit complaining of progressive hardening of the skin, lumbago, dysphagia and painful necrotic lesions in the fingers. He was diagnosed with severe diffuse systemic sclerosis and chronic kidney failure, pulmonary fibrosis, and myocardiopathy secondary to scleroderma. Here we discuss the severe manifestation of this disease, its complications, and its presentation in the male sex.