A case of congenital ameloblastic fibro-odontoma of the mandible

Ameloblastic fibro-odontoma is an extremely rare odontogenic tumor consisting of odontogenic epithelium, mesenchymal cells, dentine, and enamel. We present a case of congenital ameloblastic fibro-odontoma of the mandible.A 6-month-old male infant was referred to our hospital because of swelling of the mandibular molar region, present since birth. Radiographic examination revealed a well-demarcated radiolucent lesion of the mandible, containing a dental embryo and some small calcified foci.The tumor was surgically resected for a clinical diagnosis of a benign odontogenic tumor. The histologic diagnosis on examination of the surgical specimen was ameloblastic fibro-odontoma. The patient is free from disease 3 years after treatment.