Keratoconus presenting with bilateral simultaneous acute corneal hydrops.

Abstract Purpose To report a case of unknown keratoconus presenting with bilateral simultaneous acute corneal hydrops. Methods Case report. Results A case of a 12-year-old male patient with Leber congenital amaurosis (LCA) presented with sudden whitening and lacrimation for 2 days in both eyes simultaneously. At the initial examination, there were bilateral acute corneal hydrops, enophthalmic eyes and roving nystagmus. Ultrasonography revealed clear crystalline lenses and attached retina. Initial management consisted of topical hypertonic solutions, steroids and artificial tears. Conclusion Bilateral simultaneous acute corneal hydrops has not been reported before in the literature. It may be the presenting sign of keratoconus.