Ebstein’s Anomaly

Ebstein’s anomaly is a rare cardiac malformation characterized by varying degrees of dysplasia, apical displacement and insufficiency of the tricuspid valve associated with variable clinical presentation ranging from severely compromised newborns to patients who are asymptomatic into late adulthood. Displacement and dysplasia of the septal leaflet are displayed by 2D echocardiography in the apical four-chamber view and in the parasternal short-axis view, while displacement of the posterior leaflet is visualized in the parasternal long axis of the right ventricular inflow and in the subcostal views. Colour Doppler displays and quantifies tricuspid regurgitation, verifies antegrade flow across the pulmonary valve, determines patency of the ductus arteriosus and reveals direction of shunting across the atrial septum. PW and CW Doppler interrogation of tricuspid regurgitation allows noninvasive assessment of the right ventricular pressure.