Lymphangiectasies et entéropathie exsudative

The authors report the case of a 56 yr old man suffering from oedema of the inferior limbs. This oedema was secondary to a protein-loosing enteropathy of lymphatic origin. Histological examination revealed intestinal lymphangiectasia. After reviewing all the cases of secondary intestinal lymphangiectasia, the diagnosis of primary lymphangiectasia was proposed. Middle chain triglycerides administration induced clinical and biological improvement.